A frequência da Anomalia de Ebstein encontrada foi semelhante a de outros Centros. A técnica de Cone foi viável na maior parte dos pacientes. A mortalidade. Ebstein’s anomaly is a malformation of the tricuspid valve. In this defect, there is a downward displacement of the tricuspid valve (located between the upper and. Antecedentes: en la actualidad, con la ecocardiografía fetal, es pos ble confirmar el diagnóstico in utero de la anomalía de Ebstein y determinar, con certeza.

Author: Mezile Mukree
Country: Angola
Language: English (Spanish)
Genre: Relationship
Published (Last): 19 January 2006
Pages: 335
PDF File Size: 3.71 Mb
ePub File Size: 16.77 Mb
ISBN: 273-6-13706-256-6
Downloads: 2073
Price: Free* [*Free Regsitration Required]
Uploader: Aragis

In one of these cases an extremely rare association was found ostium primum ASD, pulmonary atresia and patent ductus arteriosus [PDA].

Anomalía de Ebstein en niños | HCA Healthcare

Regarding clinical presentation, five patients Ebstein’s anomaly in a patient with Down’s syndrome. An international co-operative study of cases. A descriptive statistical analysis was performed absolute and relative frequencies, mean and standard deviation. In this anomaliaa, another patient who underwent an MBT shunt died Access your health information from any device with MyHealth.

The electrocardiogram can reveal right atrial hypertrophy, right bundle branch block, and supraventricular tachycardia. Are you a health professional able to prescribe or ebtein drugs? Mean hospital stay was Ebstein’s tricuspid anomaly and Down’s syndrome.

Anomalía de Ebstein en niños

A new reconstructive operation for Ebstein’s anomaly of the tricuspid valve. Prognosis Asymptomatic patients, and patients with mild forms of the disease, have a normal life expectancy.


Manage Your Care From Anywhere. We are working closely with our technical teams to resolve the issue as quickly as possible. Mean cardiothoracic index was 0. Clinical and echocardiographic features of Ebstein’s malformation in Sudanese patients.

Mostrar mais Mostrar menos. Although associations between EA and certain genetic syndromes have been described, mainly trisomy 21 and Ebsteib syndrome, 9,14 these syndromes were not found in the present series. We analyzed all patients diagnosed with congenital heart defects.

Specialised Social Services Eurordis directory.

Ebstein’s anomaly in children: A single-center study in Angola | Revista Portuguesa de Cardiologia

Cone reconstruction was viable in the majority of patients, with good early and short-term results. On the other hand, Arizmendi et al. Causes Symptoms Diagnosis Treatments. All patients underwent surgical intervention. Patients with minor forms of the disease remain asymptomatic or may present with an incidental murmur, exertional dyspnea, fatigue, or palpitations. New York Heart Association.

There was a problem providing the content you requested

Detailed information Professionals Clinical practice guidelines Deutsch Ebsteein authors declare that they have followed the protocols of their work center on the publication of patient data.

We aimed to describe the frequency, clinical profile, and early and short-term post-operative results in patients under the age of 18 years operated for this anomaly in a tertiary center in Angola. For all other comments, please send your remarks via contact us.


The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. Mean cardiothoracic index decreased to 0. Differential diagnosis The major differential diagnosis, particularly during fetal life, is dysplasia of the leaflets of the tricuspid valve.

In these patients, the mean bypass time was J Am Coll Cardiol, 23pp. All patients were operated: In this defect, there is a downward displacement of the tricuspid valve located between the upper and lower chambers on the right side of the heart into the right bottom chamber of the heart or right ventricle.

This result contrasts with those of Anderson 9 and Da Silva, 15 who report a slight predominance of males, and with other studies that described no predominance of either gender.

Cardiothoracic index, echocardiographic findings, surgical indications, surgery performed and early post-operative evaluation.

Cone reconstruction was viable in the majority of patients, with good early and short-term results. Medical treatment relies on inotropic agents in case of cardiac failure and antiarrhythmic drugs in case of tachyarrhythmia.

New York Heart Association.